Abstract. ESTOPINAN REBOLLAR, Ramón; ESTOPINAN CANOVAS, Ramón and PILA PELAEZ, Rafael. Enfermedad de Hirschsprung en un adulto. Rev Col. Resumen. LOMBANA, Luis Jorge y DOMINGUEZ, Luis Carlos. Surgery in adult Hirschsprung’s disease. Rev Col Gastroenterol [online]. , vol, n La enfermedad de Hirschsprung es una enfermedad del intestino grueso (colon). Normalmente, las heces fecales son empujadas a través del colon por.

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No abnormalities resulted from the rectal examination. Treatment is always surgical.

You can change the settings or obtain more information by clicking here. Observing the Meissner and Auerbach plexus with immunohistochemical techniques and enolase S, loss of neurons ganglion cells and lower density of such plexuses were observed with respect to a normal colon Figs. The authors declare that there is no conflict of interest.

Vólvulo en adultos

Hirschsprung disease is certainly diagnosed after birth. A full-thickness biopsy was taken from the wall of the rectum, with the following findings: Laboratory studies revealed leukocytosis with left deviation and elevated C-reactive protein.

Its pages are open to the members of the Association, as well as to all members of the medical community interested in using this forum to publish their articles in accordance with the journal editorial policies. Symptoms had worsened in recent months, prompting her to seek the evaluation of a proctologist.


J Forensic Sci ; Abdomen was very distended and tympanic, with previous laparotomy scar, painful on palpation diffusely. With diagnostic methods already established in the literature, the sole treatment is surgery. Hirschsprung disease and hypoganglionosis in adults: Frequency of motor alterations detected through manometry There was neuronal dysplasia with scarce presence of ganglion cells on both edges of resection. It is important to consider the presence of this rare pathologic process in young adult patients with treatment-refractory chronic constipation, in whom other more common diseases have been ruled out through easily accessed studies, such as imaging or anorectal physiology studies.

Enfermedad de Hirschsprung en un adulto

The diagnosis of HD is supported by barium enema studies, anorectal manometry and rectal biopsy. The treatment is surgical, removing the aganglionic segment and restoring continuity of digestive tract. J Pediatr Surg ; Contents by Year, Volume and Issue. Please cite this article as: We can conclude that HD is a rare entity in adults and should be suspected in patients with megacolon with a history of constipation refractory to treatment since childhood.


Cirugía en la enfermedad de Hirschsprung del adulto

Discussion Hirschsprung’s disease affects about 1 in 5, live births and usually presents in neonatal period. H-E stain x in which no ganglion cells are observed. Hirschsprung’s disease in a young adult: Enfermedad de Hirschsprung del adulto. Under a Creative Commons license. Rev Argent Resid Cir. However, post-operative bowel functioning is not always satisfactory. C Surgical margin with ganglion cells. Based on the length of the affected segment, it is classified as: Some authors have maintained that Hirschsprung’s disease in adults probably correspond to congenital cases not diagnosed previously, and consequently it is likely that, in fact, adult Hirschsprung’s disease does not really exist as an independent entity.

Chromogranin detection of neuroendocrine cells: A resection of distal rectal mucosa of the aganglionic segment is performed, maintaining muscular wall of this segment.